Macrophage activation syndrome in a patient with systemic juvenile idiopathic arthritis
نویسندگان
چکیده
منابع مشابه
Posterior reversible encephalopathy syndrome complicating macrophage activation syndrome in a patient with systemic juvenile idiopathic arthritis
Machrophage activation syndrome (MAS) is a rare and potentially fatal disease, commonly associated with chronic rheumatic diseases, mainly juvenile idiopathic arthritis. It is included in the group of secondary forms of haemophagocytic syndrome, and other causes are lymphoproliferative diseases and infections. Its most important clinical and laboratorial manifestations are non-remitting fever, ...
متن کاملMacrophage activation syndrome in a patient with systemic onset of the juvenile idiopathic arthritis
Systemic onset juvenile idiopathic arthritis (sJIA) is defined as arthritis affecting one or more joint usually in the juvenile age group (< 16 years of age) with or preceded by fever of at least 2 weeks duration that is documented to be daily ("quotidian") for at least 3 days which may be associated with evanescent (non-fixed) erythematous rash or generalized lymph node enlargement or hepatome...
متن کاملMacrophage activation syndrome in an inadequately treated patient with systemic onset juvenile idiopathic arthritis.
Macrophage activation syndrome is a rare and potentially life threatening complication of childhood rheumatic disorders. It is described most commonly with systemic onset juvenile idiopathic arthritis (soJIA). The major clinical manifestations are non-remitting fever, hepatosplenomegaly, lymphadenopathy, bleeding diathesis, altered mental status and rash and may mimic a fl are of soJIA. The cha...
متن کاملMacrophage Activation Syndrome as the First Presentation of Juvenile Idiopathic Arthritis
Macrophage activation syndrome (MAS) is a rare feature of rheumatic disorders in children and adolescence and its presentation as the first symptom of rheumatic disorders is very infrequent. A 9-year-old girl, in whom MAS developed, was admitted to our Hospital in Tehran, Iran. She suffered from high grade fever and rash followed by multiple joint swelling months afterwards. Bone marrow aspira...
متن کاملA case of macrophage activation syndrome in a child with systemic juvenile idiopathic arthritis
Results History of the disease: the beginning of the disease was characterized with erythematosis rash and febrile temperature. Infectious diseases were excluded. Therapy with 10 mg of prednisolone per day had a temporary positive effect. However, varicella relapse with recurrent fever took place 3 weeks after. The following symptoms have been reported: fever up to 39.0C, a rash on the upper li...
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ژورنال
عنوان ژورنال: Revista Brasileira de Reumatologia (English Edition)
سال: 2015
ISSN: 2255-5021
DOI: 10.1016/j.rbre.2014.02.020